March 2013

Volume 30, Issue 1

Rare diseases with oral components: care course and quality of life

Authors: S. Toupenay N. Razanamihaja A. Berdal M-L. Boy-Lefèvre
doi: 10.1922/CDH_2811Toupenay05


Aim: To describe links between the care course of individuals suffering from rare diseases and socio-behavioural risk factors and to ascertain the impact of dental conditions on the quality of life. Design: A cross–sectional comparative study involving self-reported questionnaire was performed. Care course was evaluated using Predisposing, Enabling and Needs factors. The impacts of dental conditions on quality of life were measured with the OHIP 14 questionnaire. Proportions were compared by Chi-square test. Logistic regression for multivariate analysis assessed statistical association between variables. Results: Responses were received from 355 subjects (mean age 36.9 years, 67.6% females). Thirty-three rare diseases were recorded. Respondents were classified as group A, individuals suffering from rare diseases with a dental component (n=207, 58.3%), and group B, without dental component. Group A reported earlier diagnosis, more positive attitude toward dentists, functional limitation and higher prosthetic treatment needs. Only 17.4% of subjects having fewer than 20 teeth wear prosthetics. A higher percentage of individuals claiming pain, physical disability, psychological discomfort and social disability, was found among group B (p<0.001). Logistic regression analysis retained two impact factors: psychological disability (Exp(B)=8.66; 95% CI 1.86-40.34) and social wellbeing (Exp(B)=0.06; 95% CI 0.02-0.215). Conclusion: Rare diseases with a dental component benefited from earlier identification of symptoms. Dentists could contribute to patients’ quality of life by helping in early diagnosis, reducing functional limitation and improving social wellbeing. Key words: rare diseases, stomatognathic diseases, dental care, quality of life


Other articles in this issue

Article Pages Access
Editorial - The British Association for the Study of Community Dentistry at forty: our professional project 2-4 Download
Acknowledgement of Referees 5-5 Download
Dental Public Health in Action - Challenges encountered when conducting a dental health needs assessment of older people resident in care homes: experience from England 6-9 Download
Rare diseases with oral components: care course and quality of life 10-14 Download
Fluoridation and dental caries severity in young children treated under general anaesthesia: an analysis of treatment records in a 10-year case series 15-18 Download
Measuring determinants of oral health behaviour in parents of preschool children 19-25 Download
The self-reported oral health status and dental attendance of smokers and non-smokers 26-29 Download
Attitudes towards the use of fluorides for oral health among Islamic clerics in Kelantan Province, Malaysia 30-33 Download
The views of examiners on the use of intra-oral photographs to detect dental caries in epidemiological studies 34-38 Download
Caries experience and treatment need in adults with intellectual disabilities in two German regions 39-44 Download
Attitudes towards establishing a daily supervised school-based toothbrushing programme - determined by Q-sort methodology 45-51 Download
Oral health literacy comparisons between Indigenous Australians and American Indians 52-57 Download
Associations between oral health and height in an Indigenous Australian birth cohort 58-64 Download


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